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Home >
Product > Antibody > HEXA Monoclonal Antibody
HEXA Monoclonal Antibody
HEXA Monoclonal Antibody
Product Summary
Size:
50μL
Clonality: 3F10
Host: Mouse
Reactivity:Human
Applications: WB,FCM
Product Summary
Size:
50μL
Clonality: 3F10
Host: Mouse
Reactivity: Human
Applications: WB,FCM
Product overview
Code
BT-MCA3891
Host
Mouse
Isotype
Mouse IgG2b
Size
50μL
Clonality
3F10
Immunogen
Purified recombinant fragment of human HEXA expressed in E. Coli.
Formulation
Purified antibody in PBS with 0.05% sodium azide
Storage
Store at 4°C short term. Aliquot and store at -20°C long term.
Background
This gene encodes the alpha subunit of the lysosomal enzyme beta-hexosaminidase that, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Beta-hexosaminidase is composed of two subunits, alpha and beta, which are encoded by separate genes. Both beta-hexosaminidase alpha and beta subunits are members of family 20 of glycosyl hydrolases. Mutations in the alpha or beta subunit genes lead to an accumulation of GM2 ganglioside in neurons and neurodegenerative disorders termed the GM2 gangliosidoses. Alpha subunit gene mutations lead to Tay-Sachs disease (GM2-gangliosidosis type I).
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